González-Ramos LA, López-Cervantes G, Ruíz-Bustamante NP

Language: Spanish
References: 16
Page: 87-94
PDF size: 42.58 Kb.

ABSTRACT

Introduction: Hypoplastic left heart syndrome (HLHS) is a malformation that has a clinical manifestation in neoborns and has a high mortality rate.
Objectives: We present our experience, diagnosis and clinical follow-up at the Hospital Infantil del Estado de Sonora.
Material and Methods: We revised 21 clinical records of patients, only four had echocardiogram and 18 where by autopsy.
Results: Twenty cases studied were newborn and one preterm. Clinical symptoms were unspecified and most frequent signs registered, respiratory distress. Hepatomegaly, murmurs and abnormal peripheral pulses. Echocardiogram permitted to diagnose in intrauterine and extra uterine life.
In 18 anatomical pieces (hearts) we found atrioventricular connection, normal venous flow, arterial ventricule, and the classic hyplasic left ventricule. An aortic valve atresia was found in 89% of all cases.
Conclusion: The diagnosis for left heart syndrome is made by echocardiogram; still the outcome has a high mortality. We hope to offer other treatment alternatives by surgical palliative measures or transplant in the future. The cycle of life limit in our cases were linked to the cultural and socioeconomical status.

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