2010, Number 1
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Rev Mex Cir Pediatr 2010; 17 (1)
Biliary Tract malformation in pediatrics Choledochal Cyst
Jiménez-y Felipe JH
Language: Spanish
References: 37
Page: 11-18
PDF size: 506.95 Kb.
ABSTRACT
Introduction: Billiary tract malformation is rarely seen in pediatrics. However, choledochal cyst is the most frequent. Its diagnosis must be validated using image studies, which will provide an early surgical treatment and the prevention of the most life-threatening complication, hepatic cirrhosis.
Objective: Evaluate our experience in the management of choledochal cyst in children in the Hospital Infantil del Estado de Sonora, México.
Material and Methods: Retrospective studies of 9 cases of choledochal cyst were studied. The variables were age, sex, family background, clinical signs, laboratory exams and X-rays and the surgical treatment. The mortality is reviewed.
Results: Frequencies for boys and girls were 16.67% and 83.33%, respectively. Newborn to 11 years old was the age range considered in this study. The clinical signs were abdominal pain, infrahepatic mass and jaundice. The liver tests were abnormal. The diagnosis was verified through gastroduodenal series, hepatic ultrasound and TAC. Nine patients were under surgical cholecyst-cystectomy and the intestinal anastomosis in Y-Roux. Only one patient died.
Discussion: We presented some theories of pathogenesis of the choledochal cyst; the importance of the normal bilio-pancreatic union and the pressures within these small ducts in order to prevent the reflux of the enzymes. The risk of cancer it is discussed.
REFERENCES
Bogarín Vigo Robert Alberto. Tesis Quiste de Colédoco. Experiencia en el servicio de cirugía pediátrica del Hospital Nacional Guillermo Almenera Irigoyen. 2004; Lima, Perú.
Dong Q, Jiang B, Zhang H, et. al. Management strategy for congenital choledochal cyst with co-existing intrahepatic dilation and aberrant bile duct as well as other complicated biliary anomalies. Yansei Medical Journal 2006; 47(6):826-832.
Spitz L. Experimental production of cystic dilatation of the common bile duct in neonatal lambs. Jour Ped Surg 1977; 12:39
Tsang TM, Tam PKH, Chamberlain P. Obliteration of the distal bile duct in the development of congenital choledochal cyst. Jour Ped Surg 1994; 29(12):1582-1583.
Besner GE, Paddock HN, Kay SM. Choledochal cyst: Surgical perspective. E medicine. http://emedicine.medscape.com/article/934267-print. 29-Mayo-2009
Landig BH, Considerations of the pathogenesis of neonatal hepatitis, biliary atresia and choledochal cyst. The Concept of the infantile obstructive cholangiopathy. Progr Ped Surg 1964; 6:113
Yamataka A, Kato Y, Miyano T. Biliary tract disorders. In: Holcomb III GW, Murphy JP Ascrafth’s Pediatric Surgery, Ed. Saunders 5a ed, pp 557-577.
Escobar AJ, Aguirre GJ, Durán MA. Malformación de la placa ductal en el desarrollo de la fibrosis hepática congénita. Un estudio inmunohistoquímico. Rev Med Hosp Gen Mex 2001; 64(4):201-204.
Ramos MME, Bastidas RBE, Carrillo PMC. Marcadores Séricos de fibrosis hepática. Investigación Salud 2005; 7:61-63.
Santíes GMD, Gálvez GFJ, Meza GE, Armendáriz BJ. Fibrosis Hepática. El papel de las metaloproteínasas y de TGF-b. Gac Med Mex 2005; 141(4):315-322
Il-Han L, Gwang-Jun K. Fetal choledochal cyst diagnosed at 22 weeks of gestation by three-dimensional ultrasonography: A case report. J Korean Med Sci 2008; 23:909-911.
Marcos CA. Diagnóstico prenatal de quiste de colédoco. Presentación de un caso. Rev Arg de Ultrasonido 2008; 7(1):53-56.
Yeung CK, Lee KH, Tam YH. Lapaproscopic Excision of chodelochal cyst with hepaticojejunostomy In: Bax MA, Gerogeston KE, Rothenberg SS, Valla JS, Yeun CK editors. Endoscopic surgery in infants and children. New York: Springer, 2008 pp. 431-438.
Jona JZ, Babbit DP, Starshak RJ, et. al. Anatomic observations and etiologic and surgical consideration in Choledochal Cyst. Jour Ped Surg 1979; 14(3):315-320.
Todani T, Watanabe Y, Toki A, et. al. Reoperation for congenital Choledochal cyst. Ann. Surg. 1987; 207(2):142-147.
Ramírez AMJ, Nieto ZJ, Valencia MP. Fibrosis hepática congénita asociada a quiste de colédoco. Bol Med Hosp Infant Mex 1989; 46(12):803-807.
Nakajo T, Haschizume K, Saeki M, Tsuchida Y. Intussusception type antireflux in the Roux-en-Y loop to prevent ascending cholangitis after hepatic portojejunostomy. Jour Ped Surg 1990; 25(3):311-314.
Todani T, Urushihara N, Watanabe Y, et. al. Pseudopancreatitis in choledochal cyst in children: Intraoperative study of amylase levels in the serum. Jour Ped Surg 1990; 25(3):303-306.
Saing H, Han H, Chan KL, et. al. Early and late results of excision of choledochal cyts. Jour Ped Surg 1997; 32(11):1563-1566.
Alvarado GR, Reza VA, Uiribe RD, Gallego GJE. Quiste gigante de colédoco. Informe de un caso pediátrico. Cir Ciruj 2002; 70:40-43.
Jaunin ST, Stahelin MJ, Knuchel J, Gnehm HE. Apair of monozygotic twins anomalous pancreaticobiliary junction and pancreatitis. Jour Ped Surg 2002; 37(10):1485-1487.
Che TH, Cheng MT, Lin YL. Antenatal diagnosis of cnoledochal cyst: A case report. Changhua J Med 2003; 8(3):186-188.
Chanis AR, Norte G, Trotiño CM, Forero I. Quiste de Colédoco: Evolución, evaluación y tratamiento. Rev Hosp Niño Panamá 2005; 21(2):174-178.
Delgadillo TGH, González RF, Velázquez GA, et. al. Experiencia en el manejo de los quistes de los conductos biliares. Cirujano General 2005; 21(3):218-221.
González FMG, Solórzano MSA, Choque CC. Pseudoquiste meconial. Reporte de un caso. Anales de Radiología México 2006; 3:239-243.
Ledesma BL, Álvarez R, Marugán MSJM. Colestasis aguda y quiste de colédoco tipo IVa. Apropósito de un caso. Bol Pediatr 2006; 46:51-55.
Ahmad ALR, Bassam S. Choledochal cyst in children an experience at the royal medical service. JRMS 2006; 13(2):67-70.
CliftonMS, Goldstein RB, Slavotinek A, et. al. Prenatal diagnosis of familial type I Choledochal cyst. Pediatrics 2006; 117(3):596-600.
Pereira CN, Benavides TJ, Espinoza GC, Rostion ACG. Quiste de colédoco en pediatría: Una revisión de la literatura. Revista Pediatría electrónica 2007; 4(3). http://www.revistapediatria.cl/vol4num3/ 7.html 29-Mayo.2009.
Prochozka R, Ojeda M, Cedron H et. al. Quiste de colédoco en la gestación y puerperio: Reporte de dos casos y revisión de la literatura. Rev Gastroenterl Perú 2007; 27:71-76.
Toiber LM, Cervantes CJ, Golffer RCE, et. al. Colecistectomía laparoscópica en pacientes pediátricos. Cirujano General 2007; 29(3):202-206.
Moo KAng Ch, Sang Chi H, Jin Hyeung W, et. al. The first Korean experience of telemanipulative robot-assited laparoscopic Cholecystectomy using the da Vinci System. Yonsei Medical Journal 2007; 48(3):540-545.
Uribarrena AR, Reventós JN, Fuentes J, et. al. Diagnóstico y tratamiento de los quistes de colédoco. Presentación de 10 nuevos casos. Rev Esp Enfer Dig (Madrid) 2008; 100(2):71-75.
Ridaura SC. La biopsia hepática. Acta Pediatr Mex 2008; 29(4):216-226.
Sinha CK, Haddad M. Robot-assisted surgery in children: current status. J Robotic Surg 2008; 1:243-246.
Al-Bassam A. Robotic-assisted surgery in children: advantages and limitations. J Robotic Surg Published on line 10 April 2010 http://www.springerlink. com/content/98k723856232q520/fulltext.pdf 2-Mayo-2010
Martínez OJL, Niño SJ. Quiste de colédoco en adultos. Cir Ciruj 2010; 78:61-66.