Mora-Rico K, Romero-Montes VE, Camacho-Coronado R

Language: Spanish
References: 14
Page: 181-186
PDF size: 60.71 Kb.

ABSTRACT

Introduction: intersex syndromes constitute or sexual ambiguity in pediatric surgery a complex problem and often is an emergency that must be resolved in the neonatal period, however, some groups are diagnosed in adolescence or during adulthood.
Intersex disorders are divided into four groups and it is rare that the intersex pseudohemafroditismo is presented as a male, where female external genitalia were observed in male gonads and Mullerian duct derivatives are absent or rudimentary.
Case report: We report a case of a teenage girl 12 years of age diagnosed with Syndrome Androgen Insensitivity as a finding during an inguinal hernia.
He was admitted with a diagnosis of right inguinal hernia, laparoscopic approach to finding a closed deep inguinal ring without the presence of hernia sac, it was decided to perform inguinal approach, finding as a finding testicular characteristics and age-appropriate size in the inguinal canal.
Subsequently new laparoscopic exploration is done by finding absence of uterus and ovary structure appears to be left, at which it takes testicular tissue biopsy reports.
Discussion: Disorders of sexual differentiation or intersex require a multidisciplinary assessment for sex assignment, since it depends on the patient’s future life, both in its function, social role, and the possibility of reproduction.
The intersex is not a problem of sexual identity in the patient, as they have assumed a sex (male or female) that he is not in doubt and not a psychological problem, because the patient has no perception of belonging to a third sex.
Pediatric surgeon in this situation should begin without a multidisciplinary study aimed at determining the true sex of the patient and direct role will be to perform gonadectomy and vaginoplasty.

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