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Instituto Nacional de Neurología y Neurocirugía

2008, Number 3

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Arch Neurocien 2008; 13 (3)

Cerebellar hemanngioblastoma associated with an arteriovenous malformation and cerebral hemorrage at the puerperium

Tena SML, Salinas LC, Assia S, Rembao BD, Gómez AJL

Language: Spanish
References: 34
Page: 208-213
PDF size: 147.20 Kb.


ABSTRACT

Hemangioblastoma is a rare and uncommon quistic brain tumors, these kind of tumors are more frequently seen in male adults. It rarely invade neighbor structures and are associated to the Von Hippel-Lindau syndrome. We present the case of an 18 year old woman who presented immediately partum with an intense headache and unconscious, with data of hydrocephaly. The CT-scan showed a cystic lesion in the cerebellum, specifically the right lobe; the lesion was consistent with a hemangioblastoma. The patient was submitted to surgery, and the complete tumor extraction was satisfactory. Afterwards she presented cerebellous herniation and brain edema. The autopsy reveals hemorrhage in the right lobe of the cerebellum with abundant and irregular blood vessels which were consistent with an arteriovenous malformation. There was no residual tumor. Other findings such as uterine, pulmonary and cardiac thrombosis were also reported during the autopsy as well as Acute Respiratory Insufficiency. The coexistence of cerebellar hemangioblastomas with arteriovenous malformation accompanied by symptoms beginning in the immediate puerperium and small pancreatic cystic lesions, which are seen in the Von Hippel-Lindau syndrome, is being discussed. Few cases have been reported till today in the international accepted literature.


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