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2018, Number S1

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Acta Pediatr Mex 2018; 39 (S1)

Current treatment of classic galactosemia

López-Mejía L, Vergara-Vázquez M, López-Olivan F, Guillén-López S

Language: Spanish
References: 21
Page: 75-80
PDF size: 305.30 Kb.


ABSTRACT

Classical galactosemia is an inborn error of carbohydrate metabolism, recent evidence suggests that starting early diet treatment can successfully reverse complications of this disease. Nutritional treatment has changed over the last 20 years, currently a galactose restricted diet is recommended for a lifetime, the main sources of galactose such as milk and dairy products, as well as organ meats, meat by products and fermented soy products are not allowed. Permitted foods are all kinds of fruits, vegetables, legumes (including products based on non-fermented soybeans), oilseeds, animal products, and additives such as sodium and calcium caseinate. Calcium and vitamin D must be monitored as part of the follow-up. Nutritional education is important to patients and their families in order to maintain a lifetime diet restriction.


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