Fortis-Olmedo LL, Zumaya-Mancilla G, Popoca-Mondragón X, Téllez-Vidal D

Language: Spanish
References: 21
Page: 137-140
PDF size: 364.71 Kb.

ABSTRACT

Klippel-Feil syndrome is a rare disease, characterized by congenital fusion of two or more cervical vertebrae and can be associated with multiple systems abnormalities such as thoracic and lumbar spines malformations, in addition to lung function alterations. Physiological changes during pregnancy increases the complexity in airway management, thus when both conditions are associated is a true challenge for the anesthesiologist. We present the case of a nulliparous 23-year-old woman with type III Klippel-Feil syndrome, severe pulmonary hypertension at 30.6 weeks of gestation programed for elective cesarean and tubal ligation surgery. She presents a possibly difficult airway much like severe scoliosis to the lumbar and dorsal spine. An epidural block was considered for first elect choice for anesthetic. However, after a fail attempt of this technique, it was decided to opt for a subarachnoid block, supplying an adequate anesthetic during the surgery.

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