2005, Number 2
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Bol Clin Hosp Infant Edo Son 2005; 22 (2)
Juvenile dermatomyositis a 7 cases report
Ibarra-Silva R, Hurtado-Valenzuela JG, Sotelo-Cruz N, Uriarte-Félix JL
Language: Spanish
References: 20
Page: 102-106
PDF size: 51.91 Kb.
ABSTRACT
Introduction: Juvenil Dermatomyositis (JDM) is an idiophatic, inflammatory, sistemic disease, wich conditions to a progresive muscular weakness and characteristic exantenec, wich a tardy diagnosis and treatment has a high morbi-mortality.
Objective: To report JDM in 28 years of work at the Hospital Infantil del Estado de Sonora and to know the clinical aspects and epidemiology.
Material and Methods: We revised the clinical records with the diagnosis for JDM in the Internal Medicine Service using a concentration sheet, with the following variables: age, gender, time of appareance, clinical signs, laboratory findings, treatment and evolution.
Results: We present 7 cases with JDM in wich females predominated, the average age was 10 years old, with the characteristic clinical signs of JDM. CPK enzymes elevation was determinant for diagnosis. All cases were treated with prednisone and had a good response.
Conclusions: JDM is a rare pediatric disease and the lack of it’s knowledge can lead us to a tardy diagnosis and treatment with a high risk of complications and crippling discapacities, thus early diagnosis and treatment can improve the quality of life for this kind of patients.
REFERENCES
Bohan A, Peters JB. Polimyositis and Dermatomyositis. N Engl Med 1975; 292: 344-7.
Turner TL, Boom JA, Keyes RS, Brady RC, cols. Dermatomyositis Pediatrics in Review. 2000; 21: 389-92.
Oski’s Pediatrics principales and practice. Ed Lippincott Williams and Wilkins, Philadelphia, USA. 1999: 2166-9.
Pachman LM. Dermatomiositis Juvenil. Fisiología y expresión de la enfermedad. Pediatr Clin North Am. 1995; 92: 1071-98.
Pachman LM. Dermatomiositis Juvenil. Texbook Pediatrics Nelson. Ed Sauders Company. EU. 2000: 717-9.
Faure FMA, Rodríguez SR, Sienra MJ, Del Rio NB, cols. Dermatomiositis Juvenil: Características clínicas e inmunológicas. Bol Med Hosp Mex. 1993; 50: 717-25.
Cassidy JT, Petty RD. Pediatric Rheumatology. Juvenile Dermatomiositis. 2da. Ed. New York: Churchill-Livingstone, 1991: 331-75.
Rodriguez HR, Reynes MIN. Dermatomiositis Juvenil. Medicina Interna Pediátrica. Ed México: Interamericana Mc Graw Hill; 1997: p. 372-88.
Burgos VR, Vásquez MJ, Gómez GM. Estudio clínico de la Dermatomiositis de inicio en la infancia. Bol Med Hosp Infant Mex. 1987; 44: 463-70.
Reynes MJN, Rodríguez HR, Loredo AA y cols. Aspectos clínicos y terapéuticos de la dermatomiositis juvenil. Bol Med Hosp Infant Mex. 1994; 51: 256-66.
Laskin BJ. Novel Gastrointestinal Tract Manifestacion in Juvenile Dermatomyositis. J Pediatr. 1999; 135: 371-4.
Rider LE, Miller FW. Clasification an Treatment of the Juvenile Idiopathic inflamatory miopathies. Rheum Dis North Am. 1997, 23: 619-55.
Mitchell JP, Dennis GJ. Juvenile Dermatomyositis presenting with anasarca: A possible indicator of severe disease activity. J Pediatric. 2001; 138: 942-5.
Arenas R. Dermatomiositis. Dermatología-Atlas, diagnóstico y tratamiento. Ed McGraw-Hill. Méx. DF. 1987: 140-3.
Bowyer SL, Ragsdale CG, Sullivan DB. Childhood Dermatomyositis: Factor predicting funtional outcome and develoment of dystrophic calcification. J Pediatr. 1983; 103: 8882.
Dalakas MC. Polimyositis, Dermatomyositis and inclusion body myposisitis. N Engl J Med. 1991; 325: 1487-98.
Targoff ON. Myositis and Myopathies. current Opinion in Rheumatology. 1999; 11: 453-5.
Miranda M, Carballo A. Dermatomiositis Juvenil: Manifestaciones clínicas y de laboratorio, Rev Chil Pediatr. 1991; 62: 28-33.
Tanimoto K, Nakama K, Kano S, cols. Criterios de clasificación de la polimiositis y dermatomiositis. The Journ of Rheumath. 1995; 22: 4.
Lauren M, Pachman MD. Rheumatic Disease Clinics of North America. Dermatomiositis Juvenil: Inminogénetica, Fisiopatología y Manifestaciones Clínicas. Núm. 3-2002: 495-515.
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