Moya-Jiménez S, Lozano-Corona R, Gómez-Ríos N, Rodríguez-Ortega MF, Carrasco-González H

Language: Spanish
References: 22
Page: 99-105
PDF size: 216.63 Kb.

ABSTRACT

Introduction. Marfan syndrome is an inherited connective tissue disorder involving the heart and great vessels before surgery was accounted for 90% of mortality in these patients.
Objective. To report the effectiveness of hybrid treatment in Marfan syndrome.
Case report. Female patient 40 years old, carrying Marfan syndrome, diagnosed with aortic valve prolapse and an aneurysm of the ascending aorta, performing a modified procedure Bentall-De Bono. Descending thoracic aneurysm, standing thoracic stent (TEVAR). Aneurysmal dilation of the aorta below renal, taking both iliac arteries, placing grafts aorto-bifemoral polytetrafluoroethylene.
Results. With the use of hybrid treatment the patient is clinically asymptomatic currently can perform activities of daily life.
Conclusions. The treatment of choice for cardiovascular level in this condition is surgical repair, endovascular therapy being a reliable tool in specific cases; thus forming a hybrid approach which aims to reduce morbidity and mortality involved in open processes.

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