Palafox D, Arrieta-Joffe P, Cárdenas-Mejía A

Language: Spanish
References: 18
Page: 136-144
PDF size: 458.44 Kb.

ABSTRACT

Möbius syndrome is characterized by bilateral facial and abducens nerve paralysis. Between January 2008 and July 2013, 165 patients were treated at the Facial Paralysis and Peripheral Nerve at the Clinic Plastic and Reconstructive Surgery Division at «Dr. Manuel Gea González» General Hospital, 38 patients (22%) were diagnosed with Möbius syndrome. Only 30 cases underwent a reconstructive procedure. 22 (58%) were classified as complete Möbius, 12 (32%) had incomplete Möbius and 4 (11%) were Möbius-like. The mean age was 13.7 years. Surgical procedures included: free gracilis transfer: 15 cases (50%), temporal muscle transposition: eight cases (26.6%) and nerve transfers: seven cases (23.3%). Preliminary results demonstrate that the treatment with free muscular transfer favors a better commissure excursion, complete oral competence and improved feeding and speech. An improvement in facial expression aids the patients self-esteem and sociability.

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