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Academia Mexicana de Neurología, A.C.

2010, Number 4

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Rev Mex Neuroci 2010; 11 (4)

Neuropsychological abnormalities in multifocal motor neuropathy with conduction block

Ruiz-Sandoval MC, Reséndiz-Ramírez Y, Villaseñor-Cabrera T, Álvarez-Palazuelos LE, Chiquete E, Ruiz-Sandoval JL

Language: Spanish
References: 26
Page: 302-305
PDF size: 265.50 Kb.


ABSTRACT

Introduction: Multifocal motor neuropathy with conduction block (MMNCB) is a rare entity of autoimmune source characterized by distal asymmetric weakness with predominance in upper extremities, arreflexia and muscular atrophy. Clinical case: 31-year-old man with MMNCB at infancy onset and psico-behavioral disturbances evidenced since the adolescence. Conclusions: The presence of antigangliósido GM1 antibodies explains not only the neuropathic syndrome, but also the neuropsychological alterations; due to that GM1 also exist to a central level.


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