Bayona SP, Macotela NKA, Gómez MY, Barbero IMA, Avendańo BA, Cruz MV

Language: Spanish
References: 16
Page: 339-344
PDF size: 194.91 Kb.

ABSTRACT

The Mayer-Rokitansky-Küster-Hauser is a rare condition that affects one in every 4,000 women. It is a complex malformation that includes vaginal atresia or aplasia with other abnormalities of the Müllerian ducts ranging from absence to rudimentary uterus. Transabdominal ultrasound should be performed in first instance. Magnetic resonance imaging is a technique that provides better sensitivity and specificity than ultrasound diagnosis. The treatment must be multidisciplinary with psychological support to the patient. For the creation of the neovagina the treatment can be divided into nonsurgical as the technique of Frank and Ingram with vaginal dilators and surgical techniques as the Abbe-McIndoe, Vecchietti, Davydov, Williams vaginoplasty, colpoplastia with rectal sigmoid . We report the clinical case of a woman of 17 years old with primary amenorrhea and secondary sexual characteristics present. Pelvic ultrasound was performed which reported presence of hypoplastic uterus. Diagnostic laparoscopy was performed and found imperforate hymen, Müllerian small bulbs, normal ovaries and salpinges. We performed hymen plasty and since then conservative management has been performer in addition with urogynecology with vaginal dilation therapy and psychological support.

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