2011, Number 2
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Cir Cir 2011; 79 (2)
Atypical intermediate-grade mediastinal carcinoid. Case presentation
Carrillo-Muñoz A, Onofre-Borja M, Borrego-Borrego R, Chávez-Mercado L, Navarro-Reynoso FP, Ibarra-Pérez C
Language: Spanish
References: 14
Page: 191-195
PDF size: 435.33 Kb.
ABSTRACT
Background: Approximately 25% of carcinoid tumors develop in the respiratory system. Neuroendocrine carcinoids represent ~5% of all mediastinal tumors and 1-5% of all intrathoracic neoplasms. They contain numerous neurosecretory granules that synthesize, store and release neurohumoral substances that can induce the carcinoid syndrome.
Clinical case: A 21-year-old male presented with a rapidly progressive paraneoplastic syndrome unleashed by anacute urethritis. Two left mediastinal masses were identified and resected. Postoperative evolution has been uneventful during the first year.
Conclusions: We emphasize the importance of early detection of primary and satellite lesions of these tumors including neurohumoral markers and PET/CT scans as in this case, as well as the participation of a multidisciplinary team.
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