2006, Number 1
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Rev Mex Cir Pediatr 2006; 13 (1)
Botroides biliary tract rhabdomyosarcoma A report of a case and review of literature
Ambriz-González G, Sánchez-Zubieta F, Coello-Ramírez P, Cordero-Zamora A
Language: Spanish
References: 12
Page: 30-34
PDF size: 174.20 Kb.
ABSTRACT
Introduction: Rhabdomyosarcoma is a malignant soft tissue tumor most common in pediatric patients. The most common site involved includes head and neck, rarely found in viscera larynx, bronchi, small intestine and biliary tract. The rhabdomyosarcoma of the biliary tree in childhood is very rare.
Case report: Enter male patient 2 years with 2 weeks of evolution with jaundice, dark urine, acolia, anorexia, fever, abdominal distention and melena stools abdominal pain not localized. On admission the presumptive diagnosis of viral hepatitis and hepatic encephalopathy. Initially involved with the diagnosis of choledochal cyst vs. Caroli disease. It reinterviene in July 2002 with the following findings: The tumor fusiform choledochal cystic and common bile duct with report of gallbladder with infiltration of rhabdomyosarcoma. At present, 10 months later the patient is without evidence of recurrence
Discussion: Rhabdomyosarcoma of extrahepatic bile duct is a rare highly malignant tumor that occurs exclusively in children. Most of the cases preoperatively mistaken for Choledochal Cyst. Treatment modalities include surgical resection, radiotherapy and chemotherapy. Only with a multidisciplinary approach can prolong survival. In the case of our patient at the time evolution has remained stable, so we hope that aggressive management allows us to apply a proper survival.
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