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ISSN 2007-087X (Print)
Órgano Oficial de la Sociedad Mexicana de Ortopedia Pediátrica

2010, Number 1

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Rev Mex Ortop Ped 2010; 12 (1)

Neurofibroma plexiforme gigante del nervio ciático. Informe de caso

Sánchez-Torres LJ, Santos-Hernández M, Chávez RMM

Language: Spanish
References: 12
Page: 48-52
PDF size: 175.15 Kb.


ABSTRACT

Background: Plexiform neurofibromas are benign tumors originating from the nerve sheaths of subcutaneous or peripheral nerves, that can involve multiple fascicles, and be of great size. They occur almost exclusively in patients with neurofibromatosis type 1 (von Recklinghausen’s disease), and are lesions with malignant potential. Surgery is not applied to children with small tumors. Case report: Report a case of a 15 years old male patient with a giant plexiform neurofibroma of sciatic nerve, without neurofibromatosis. The diagnostic work-up was completed and an incisional biopsy confirmed the diagnosis, a wide resection was performed. Final pathologic diagnosis was confirmed. Results: Patient is asymptomatic, with a drop-foot gait and anesthesia in the ipsilateral foot. He does not accept or need any orthotic aid. Discussion: Resection of sciatic nerve is a controversial procedure because of the neurological complications like pressure sores and muscular deficits, that are difficult to resolve; however we opted for limb-sparing surgery with good results. Conclusions: Plexiform neurofibroma is not pathognomonic of neurofibromatosis type 1. Is necessary more time to evaluate sensitive deficit in patients with sciatic nerve resection.
Level of evidence: IV


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