2006, Number 1
<< Back Next >>
Rev Gastroenterol Mex 2006; 71 (1)
Intestinal lymphangiectasia: a forgotten cause of chronic diarrhea
Rodríguez LG
Language: English
References: 9
Page: 55-58
PDF size: 127.54 Kb.
ABSTRACT
Intestinal lymphangiectasia is a rare autosomal dominant disorder or acquired condition that leads to lymph obstruction, poor chyle transport and concomitant problems. We describe the cases of two women with chronic diarrhea in whom the common signs of lymphagiectasia-hypoalbuminemia, lymphopenia and distal edema- were found. One of them also had pleural effusion and chylous ascites. The diagnosis was performed by intestinal biopsy. We herein review the histopathologic, radiographic and endoscopic features of this disorder and case reports in Mexican population.
REFERENCES
Waldman TA, Steinfeld JL, Dutcher TF, et al. The role of the gastrointestinal system in idiopathic hypoproteinemia. Gastroenterology 1961; 41: 197-207.
Pomerantz M, Waldman TA. Systemic lymphatic abnormalities associated with gastrointestinal protein loss secondary to intestinal lymphangiectasia. Gastroenterology 1963; 45: 703-11.
Dobbins WO. Electron microscopic study of the intestinal mucosa in intestinal lymphangiectasia. Gastroenterology 1966; 51: 1004-17.
Fox U, Lucani G. Disorders of the intestinal mesenteric lymphatic system. Lymphology 1993; 26: 61-6.
Shani M, Theodor E, Frand M, Goldman B. A family with protein-losing enteropathy. Gastroenterology 1974; 66: 433-8.
Roberts SH, Douglas AP. Intestinal lymphangiectasia: the variability of presentation. A study of five cases. Q J Med 1976; 1976: 39-48.
Strober W, Wochner RD, Carbone PP, Waldman T. Intestinal lymphangiectasia. A protein lossing enteropathy with hypogammaglobulinemia, lymphocytopenia and impaired homograft rejection. J Clin Invest 1967; 46: 1643-9.
Mistilis SP, Skyring AP, Stephen DD. Intestinal lymphangiectasia: mechanism of enteric loss of plasma protein and fat. Lancet 1965; 1: 77-9.
Perisic VN, Kokai G. Bleeding from duodenal lymphangiectasia. Arch Dis Child 1991; 66: 153-4.