2015, Número 1
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Rev Mex Ortop Ped 2015; 17 (1)
Consideraciones diagnósticas en la hemihipertrofia
Colmenares-Bonilla D
Idioma: Español
Referencias bibliográficas: 37
Paginas: 39-44
Archivo PDF: 149.07 Kb.
RESUMEN
No está descrita la verdadera incidencia de la hemihipertrofia, ya que pequeñas variaciones en el tamaño de las extremidades se consideran normales; se tienen los reportes de casos de pacientes que buscan atención médica por diferencias considerables. En ocasiones es detectable desde el nacimiento si la diferencia es grande. La hemihipertrofia está clasificada como no sindrómica cuando carece de datos que lo vinculen a un síndrome genético; en el caso de la sindromática, es importante llegar al diagnóstico definitivo, debido a las diferentes implicaciones pronósticas. Entre los diferenciales más comunes resaltan la neurofibromatosis, los síndromes de Proteus, Klippel-Trenaunay Weber y Beckwith-Wiedemann.
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