Fuentes LEE, Tornes SKL, Fuentes TJC

Language: Spanish
References: 10
Page: 190-199
PDF size: 412.08 Kb.

ABSTRACT

Introduction: within the head and neck tumors, Ewing's Sarcoma is one of the least frequent, it affects the jaw and maxilla, but it is even more rare in soft tissues originated in the nasal cavity or sinuses; share characteristics with primitive neuroectodermal tumors. They usually occur in children and young adults, presenting themselves with great aggressiveness.
Case presentation: We present a 4-year-old girl who went to the office with an inflammation in the floor of the right nostril, without fever, without pain, poor rhinorrhea with right nasal obstruction.
Discussion: MRI was performed visualizing a tumor mass towards the right nasal floor, of great intensity, isointense and without rupture of the walls of the maxillary sinus or other neighboring structure. Incisional sample was taken for biopsy of the lesion that positively reports Ewing's sarcoma.
Conclusions: treatment with radiotherapy and chemotherapy was applied.

REFERENCES

1. Shweta S, Shantnu C, Rizwan A, Nalin C, Bhushan S, et al. Atypical presentation of Ewing's sino-nasal tumor: case report. European Journal of Medical Case Reports 2019; 3(1): 37-40.

2. Ewing J. Diffuse endothelioma of bone. CA: Cancer Journal for Clinicians 1972; 22(2): 95-98.

3. Rico-Ramírez O, Ornelas Ramos JR, Abbud Abbud E, Rojas Ávila VF, Figueroa Sandoval JF. Rabdomiosarcoma alveolar de presentación nasal: informe de caso. Gaceta Mexicana de Oncologia 2017; 16(3): 203-206.

4. Alfaro-Iraheta FA, López-Chavira A, Sánchez-Santana JR, Gallardo-Ollervides FJ, Juárez-Ferrer JCM, Romo-Magdaleno JA. Sarcoma de Ewing de la cavidad nasal. An Orl Mex 2018; 62(4): 235-41.

5. Riveros-Ramos LC, Velasco-Hidalgo L, Shalkow-Klincovstein J, Rojas-Maruri CM, Cárdenas-Cardos R, Rivera-Luna R. Tumor neuroectodérmico primitivo primario de páncreas en un paciente pediátrico. Reporte de caso y revisión de la literatura. Acta pediátr Méx 2016; 37(1): 26-31.

6. Ventura-Martínez N, Cebreros-Rosas D, Miragall-Alba L, Ruiz-Gutierrez JP, Puglia-Santos V. Sarcoma de Ewing extra óseo en cabeza y cuello: revisión de la literatura a propósito de un caso. Rev Esp Cir Oral Maxilofac 2017; 39(2): 105-112.

7. Villalta Fallas JC. Sarcoma de Ewing. Revista Médica de Costa Rica y Centroamérica 2015; LXXI(617): 695-704.

8. Aliaga R, Lagos S, Guerra H. Sarcoma de Ewing/tumor neuroectodérmico primitivo de la fosa nasal. Rev Soc Peru Med Interna 2018; 31(1): 35.

9. López F, Grau JJ, Medina JA, Alobid I. Consenso español para el tratamiento de los tumores nasosinusales. Acta Otorrinolaringológica Española 2017; 68(4): 226-234.

10. Baruchela S, Pappog A, Krailo M, Skort Bakerd B, Bing Wu, Doojduen V, et al. A phase 2 trial of trabectedin in children with recurrent rhabdomyosarcoma, Ewing sarcoma and non-rhabdomyosarcoma soft tissue sarcomas: A report from the Children’s Oncology Group. European Journal of Cancer 2012; 48(4): 579-85.