Ajiz PVA, Orellana AÁR, Pulido DN, Quintal RMJ

Language: Spanish
References: 10
Page: 182-184
PDF size: 496.22 Kb.

ABSTRACT

Brunsting-Perry pemphigoid is considered a localized subtype of scarring pemphigoid. It is characterized by subepidermal blisters predominantly on the head and neck, rarely affecting mucous membranes. These blisters can heal with atrophic scars. It is a rare and clinical manifestations are usually nonspecific. Sequels such as scarring alopecia can be observed when the scalp is involved. Immunofluorescence shows linear deposits of igg and c3 along the basal membrane. Recently it has been reported the identification of autoantigens directed not only towards elements of the lamina lucida, but also to the sublamina dense, linking it as a variant of other subepidermal bullous dermatoses.
We present a 57-year-old male with diagnosis through histopathology and immunofluorescence.

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