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2020, Number 3

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Residente 2020; 15 (3)

Limbic encephalitis secondary to relapsing polychondritis

Bravo-Ruiz OL, García-Ortega YE, Salcedo-Hernández MJ, Mireles-Ramírez MA, González-Usigli HA

Language: Spanish
References: 15
Page: 113-117
PDF size: 275.93 Kb.


ABSTRACT

Introduction: Relapsing polychondritis. (RP) is a multisystemic rheumatic disease. It is estimated that 3% of RP patients present neurological manifestations. Being limbic encephalitis one of the most important. The pathophysiology of limbic encephalitis in RP is not yet fully understood, however, patients with this manifestation have a poor prognosis for evolution. The objective of the presentation of the clinical case is to disseminate the pivotal data of a rare manifestation in order to receive timely treatment. Clinical Case: A 43-year-old male, right-handed, increased volume of both atrial pavilions with hyperthermia and palpation pain, subsequent, recent memory loss and behavioral changes, after 1 month with aphasia and seizures accompanied by stereotyped oral movements, which was approached under the diagnosis of limbic encephalitis and looking for the primary cause, the physical examination of ear pavilions was emphasized. Discussion: Limbic encephalitis in patients with RP is rare, however, there are pivotal data to make the diagnosis in a timely manner and try to delimit the damage both neurologically and systematically. Conclusions: Limbic encephalitis should be included in manifestations secondary to PR.


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