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Órgano Oficial del Colegio Mexicano de Alergia, Asma e Inmunología Pediátrica y de la Asociación Latinoamericana de Pediatría

2020, Number 2

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Alerg Asma Inmunol Pediatr 2020; 29 (2)

Atypical eye manifestation in macrophage activation syndrome complicating systemic juvenile idiopathic arthritis

García-Domínguez M, González-López E, Arce-Cabrera D, Heras-Salazar R

Language: Spanish
References: 17
Page: 66-70
PDF size: 256.34 Kb.


ABSTRACT

Macrophage activation syndrome complicating systemic-onset juvenile idiopathic arthritis is a serious and potentially life-threatening condition. Characterized of acute hyperinflammation with fever, cytopenias, multiple organ dysfunction, and hemophagocytosis in the reticuloendothelial system with increased macrophage activity. We present adolescent of a 13-year-old with systemic-onset juvenile idiopathic arthritis complicated by macrophage activation syndrome, who developed bilateral infiltrative retinochoroiditis with an ischemic vascular component and severe vision impairment.


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