Romero MRL, Smith CO, Romero RBR, Sánchez LR

Language: Spanish
References: 7
Page: 1-10
PDF size: 438.04 Kb.

ABSTRACT

Introduction: Becker's cardiomyopathy is included among the muscular dystrophies considered dystrophinopathic which affects the heart. These diseases have recessive inheritance linked to the X chromosome. Mutations in the dystrophin gene cause them.
Objective: To characterize the cardiovascular functionality of the patient treated with ergometry-guided cardiovascular kinesitherapy.
Case report: A male 26 year-old patient has a history of Becker muscular dystrophy showing dilated cardiomyopathy. Moderate functional disability was documented. Cardiovascular rehabilitation was prescribed for six weeks, with protocols at constant load and interval at 50 to 95% intensity of the physical load, and a frequency of five days per week.
Conclusion: He was first patient with Becker's cardiomyopathy treated with cardiovascular kinesiotherapy and Ergometric guidance, which was reported in Cuban and international literature. Functionally improved with respect to pharmacotherapy.

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