2019, Number 5-6
<< Back Next >>
Rev Sanid Milit Mex 2019; 73 (5-6)
Behçet disease incomplete. A case report
Cerda-Reyes S, Morales-Fernández IN, Franco-Ramírez EO, Rodríguez-Reyes A, Alcántara-Salinas A
Language: Spanish
References: 8
Page: 333-336
PDF size: 274.16 Kb.
ABSTRACT
Background: Behçet’s disease (BD) is a multisystem vasculitis with various manifestations, among which the most common is the presence of painful ulcers of more than 14 days, occurring at least 3 times a year, either alone or in combination with other injuries may occur seven years before diagnosis and sometimes present proof positive pathergy. Histopathology study with neutrophilic vascular reaction or leukocytoclastic vasculitis.
Clinical case: Patient of 14year with evolution of 3 years, with the presence of painful oral ulcers in more than three episodes a year, with biopsy oral cavity lesions compatible with BD and HLA B 51 positive. We will start treatment with immunosuppressant, mycophenolate 400 mg/m2sc for a year and prednisone 50 mg every 24 hours dose reduction with good response.
Conclusions: Chronic oral ulcers are suspected of BD sign.
REFERENCES
. Seoudi N, Bergmeier LA, Drobniewski F, Paster B, Fortune F, The oral mucosal and salivary microbial community of Behçet’s syndrome and recurrent aphthous stomatitis. 2015; 7 (27150): 1-9.
Fonseca-Cardoso A, Rocha-Filho P, Melo Correa-Lima A. Neuro-Behçet: differential diagnosis of recurrent meningitis Rev Med Chil. 2013; 141 (1): 114-118.
Koné-Paut I, Behçet’s disease in children, an overview Koné-Paut Pediatric Rheumatol. 2016; 14 (10): 1-8.
Koné-Paut I, Shahram F, Darce-Bello M, Cantarini L, Cimaz R, Gattorno M et al. Consensus classification criteria for paediatric Behçet’s disease from a prospective observational cohort: PEDBD. Ann Rheum Dis. 2015; 75 (6): 958-964.
Senusi A. Genital ulcer severity score and genital health quality of life in Behçet’s disease. Orphanet J Rare Dis. 2015; 10: 117: 1-11.
Arevalo JF, Lasave AF, Al Jindan MY, Al Sabaani NA, Al-Mahmood AM, Al-Zahrani YA et al. Uveitis in Behçet disease in a tertiary center over 25 years: The KKESH Uveitis Survey Study Group. Am J Ophthalmol. 2015; 159 (1): 177-184.
Khairallah M, Accorinti M, Muccioli C, Kahloun R, Kempen JH. Epidemiology of Behçet disease. Ocul Immunol Inflamm. 2012; 20 (5): 324-335.
Park UC, Kim TW, Yu HG. Immunopathogenesis of ocular Behçet’s. Dis J Immunol Res. 2014; 3: 1-13.