medigraphic.com

2004, Number 4

<< Back Next >>

Arch Cardiol Mex 2004; 74 (4)

Scimitar syndrome associated to pulmonary atresia with interventricular communication. First reported case

Alva C, Valero G, Martínez A, Riera C, David F, Jiménez S, Ortegón J, Sánchez A, López D, Ramírez E

Language: Spanish
References: 13
Page: 301-305
PDF size: 98.25 Kb.


ABSTRACT

We present the case of a 15 months-old male with Scimitar Syndrome associated with ventricular septal defect and pulmonary atresia. The diagnosis was made by cardiac catheterization and angiography and was confirmed by the necropsy. Clinical and surgical considerations of this exceptional association were made. To the best of our knowledge this is the first case reported in the relevant literature.


REFERENCES

  1. Neill CA, Ferencz C, Sabiston DC, Sheldon H: The familial occurrence of hypoplastic right lung with systemic arterial supply and venous drainage “scimitar syndrome”. Bull Johns Hopkins Hosp 1960; 107: 1-20.

  2. Brown JW, Ruzmetov M, Minnich DJ, Vijay P, Edwards CH, Uhlig PN, et al: Surgical management of scimitar syndrome: an alternative approach. J Thorac Cardiovasc Surg 2003; 125: 238-245.

  3. Perry LW, Neill CA, Ferencz C: Infants with congenital heart disease: the cases. In: Ferencz C, Rubin JD, Loffredo CA. Eds. Perspectives in pediatric cardiology: Epidemiology of congenital heart disease. The Baltimore-Washington Infant Study 1981-1989. Armonk, NY: Futura Publishing Company, 1993: 33-62.

  4. Ferencz C, Loffredo CA, Correa-Villaseñor A: Malformations of the cardiac outflow tract in genetic and environmental risk factors of major cardiovascular malformations. The Baltimore-Washington Infant Study 1981-1989. Armonk, NY: Futura Publishing Co. 1997: 59-102.

  5. Honey M: Anomalous pulmonary venous drainage of the right lung to inferior vena cava “scimitar syndrome”: clinical spectrum in older patients and role of surgery. Q J Med 1977; 46: 463-483.

  6. Mardini MK, Sakati NA, Lewall DB: Scimitar syndrome. Clin Pediatr 1982; 21: 350-354.

  7. Haworth SG, Saver W, Buhlmeyer K: Pulmonary hypertension in scimitar syndrome in infancy. Br Heart J 1983; 50: 182-189.

  8. Huddleston CB, Exil V, Canter C, Mendeloff EN: Scimitar syndrome presenting in infancy. Ann Thorac Surg 1999; 67: 154-160.

  9. Azhari N, Al-Fadley F, Bulbul ZR: Tetralogy of Fallot associated with scimitar syndrome. Cardiol Young 2000; 1: 70-72.

  10. Gikonyo DK: Scimitar syndrome in neonates: report of four cases and review of the literature. Pediatr Cardiol 1986; 6: 193-197.

  11. Le Rochais JP, Icard P, Davani S, Abouz D, Evrad C: Scimitar syndrome with pulmonary arteriovenous fistulas. Ann Thorac Surg 1999; 68: 1416-1418.

  12. Brown JW, Ruzmetor M, Minnich DJ, Vijay P, Edwards C, Uhlig PN: Surgical management of scimitar syndrome: an alternative approach. J Thorac Cardiovasc Surg 2003; 125: 238-245.

  13. Calhoun RF, Mee RBB: A novel operative approach to scimitar syndrome. Ann Thorac Surg 2003; 76: 301-303.




2020     |     www.medigraphic.com