2020, Number 1
Solitary mastocytoma in pediatrics. Case report and literature review
Language: Spanish
References: 8
Page: 46-49
PDF size: 133.98 Kb.
ABSTRACT
The mastocytoma is a genodermatosis of unknown etiology, so it is included in the group of rare or uncommon diseases; it usually appears in childhood or at birth. It is characterized by local or systemic accumulation of primed cells, which causes the appearance of persistent, pigmented and very itchy skin lesions with exclusive skin involvement, usually presents as a single lesion in the neck, trunk, arms and legs. Typical features are that of a reddish-brown or yellowish brown nodule, of gummy consistency, the surface looks like orange peel, and Darier's sign. The case of a 4-month-old infant with a diagnosis of solitary mastocytoma with Darier's sign is presented. This report is made due to the low frequency of this disease at the Paquito González Cueto de Cienfuegos University Pediatric Hospital. Currently the patient is monitored by dermatology specialists, with antihistamine treatment and mast cell stabilizer.REFERENCES
De Grazia R, Apt P, Ibarra A, Sazunic I. Mastocitosis cutánea maculopapular infantil: reporte de un caso. Revista Médica Clínica Las Condes [revista en Internet]. 2019 [citado 2 Ene 2020];30(3):[aprox. 4p]. Disponible en: https://reader.elsevier.com/reader/sd/pii/S071686 4019300446?token=2064A35993AEE1F7B51100 D554CBC41E8D4106E7857B513CE97F9C1B9E10 D054D028D7EBE0C97BA9B0BDEA76B05DF5CD
Azaña JM, Torrelo A, Matito A. Actualización en mastocitosis. Parte 2: categorías, pronóstico y tratamiento. Actas Dermo-Sifiliográficas [revista en Internet]. 2016 [citado 12 May 2019];107(1):[aprox. 8p]. Disponible en: https://www.clinicalkey.es/service/content/pdf/wa termarked/1-s2.0-S0001731015004081.pdf?local e=es_ES&searchIndex=
Azaña JM, Torrelo A, Matito A. Actualización en mastocitosis. Parte 1: fisiopatología, clínica y diagnóstico. Actas Dermo-Sifiliográficas [revista en Internet]. 2016 [citado 19 Ago 2018];107(1):[aprox. 10p]. Disponible en: https://www.clinicalkey.es/service/content/pdf/wa termarked/1-s2.0-S0001731015004019.pdf?local e=es_ES&searchIndex=