Conde-Taboada A, De la Torre FC, Flórez MA, Mayo PE, González SB, Cruces PM

Language: Spanish
References: 13
Page: 169-172
PDF size: 396.18 Kb.

ABSTRACT

Epidermolysis bullosa is a collection of genetic disorders, with skin fragility and after minor trauma blistering. Dystrophic epidermolysis bullosa associates scarring, milia, and nail dystrophy, and blisters are subepidermal. Epidermolysis bullosa pruriginosa is a subtype with intense itching and lichenifi ed lesions. Albopapuloid lesions have been rarely reported associated to this type.
Case report. A 34-year-old woman refers blisters and intense pruritus since she was a child. Examination reveals scars, erosions, and isolated blisters, located mainly on limbs. Violaceous hypertrophic lichenifi ed lesions occur on dorsal arms and hands. Most fi nger and toe nails are dystrophic. Whitish papules are present on trunk. Skin biopsy shows a subepidermal blister with mild infl ammatory cell infi ltrate.
Comment. We present a case of dystrophic epidermolysis bullosa pruriginosa that associates albopapuloid lesions. These lesions are found mainly in dominant dystrophic epidermolysis bullosa, but they are not pathognomonic.

REFERENCES

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