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ISSN 2007-087X (Print)
Órgano Oficial de la Sociedad Mexicana de Ortopedia Pediátrica

2019, Number 1-3

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Rev Mex Ortop Ped 2019; 21 (1-3)

Clinical and therapeutic evolution of the hyperplasic calle in osteogenesis imperfect. Review of the literature and case report

Arenas-Díaz AL, Barrón-Torres EA, Ríos-Ruíz G

Language: Spanish
References: 10
Page: 26-31
PDF size: 229.79 Kb.


ABSTRACT

Osteogenesis Imperfecta is a spectrum of connective tissue abnormalities that affect the skeleton, ligaments, skin, sclerotics and dentin, which often leads to multiple fractures and bone deformities. The incidence is 1 in 10,000 to 20,000 live births. The objective of this study was to describe the clinical presentation, evolution and treatment used in the presence of a hyperplastic callus in osteogenesis imperfecta. Clinical case: Male of 4.7 years, who presented deformity in right femur at 3.2 years treated with osteotomies of alignment and placement of telescoped nail. Four weeks later he presents gradual volume increase and pain in the right thigh. At the sixth week, a spicular periosteal reaction was observed at the osteotomy site. Hyperplastic callus was diagnosed in the right femur and treated with steroids. Eighteen month later it presents good clinical and radiographic evolution. Conclusions: The adequate clinical and radiographic evaluation can lead us to the accurate diagnosis and rule out differential diagnoses. The use of steroid in this clinical case was effective for its clinical and radiographic control. Given the rarity of the disorder, the treatment requires multidisciplinary support.


REFERENCES

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