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2019, Number 1

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CorSalud 2019; 11 (1)

Fragmented QRS and sudden death in a patient with arrhythmogenic right ventricular dysplasia/cardiomyopathy

Rodríguez LLA, Rodríguez ME, Cruz EJM, Díaz SYM, Gavilanes HR, Quenta TRR, González AJA, Santana SC

Language: Spanish
References: 25
Page: 70-74
PDF size: 382.08 Kb.


ABSTRACT

The arrhythmogenic right ventricular dysplasia or cardiomyopathy is a genetic heart disease whose diagnosis is often a challenge for the clinician. It is one of the most common causes of sudden cardiac death in adolescence and in young adults. We present the case of a patient with a history of malignant ventricular arrhythmias and recovered sudden cardiac death due to arrhythmogenic right ventricular dysplasia, with QRS fragmentation in the right precordial leads, as a marker of the presence of a suitable substrate for the emergence of spontaneous ventricular fibrillation. The pathogenesis, diagnosis and treatment of this disease are discussed.


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