2019, Number 4
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Rev Fac Med UNAM 2019; 62 (4)
Langerhans’ cell histiocytosis in their orbitfocused presentation. Review of the topic regarding a case
Dávila MR, Figueroa FA, Ontiveros VF, Urbina SA
Language: Spanish
References: 7
Page: 30-34
PDF size: 240.12 Kb.
ABSTRACT
Objective: To describe a case of Langerhans cell histiocytosis
in a pediatric patient.
Method: A 4-year-old patient with proptosis, diplopia, fever
and loss of visual acuity, with evident image in a computed
tomography of orbital mass with bone erosion. An excisional
biopsy was performed by coronal craniotomy. The histopathological
result was Langerhans cell histiocytosis.
Results: The anatomopathological study showed a neoplasm
of small round and blue cells, compatible with Rhabdomyosarcoma.
Immunohistochemical tests concluded the diagnosis
of Langerhans cell histiocytosis.
Conclusion: Langerhans cell histiocytosis is a rare disease that
requires clinical suspicion and a timely diagnosis to adjust the
treatment and improve the survival of patients.
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