2018, Number 3
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Arch Inv Mat Inf 2018; 9 (3)
Peutz-Jeghers syndrome. Apropos of a case
Pérez-Elizondo AD, Ruíz-Pérez ME
Language: Spanish
References: 7
Page: 91-93
PDF size: 192.04 Kb.
ABSTRACT
Peutz-Jeghers syndrome is an inherited disorder which usually debuts during childhood. It is characterized by mucocutaneous pigmentation and hamartomatous polyps in the gastrointestinal tract. Numerous reports indicate a high incidence of gastrointestinal and extraintestinal cancer in these patients, their appearance at a young age, as well as its association with ovarian and testicular tumors. An aggressive approach of these patients seems to be necessary.
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