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Boletín Clínico de la Asociación Médica del Hospital Infantil del Estado de Sonora

2005, Number 1

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Bol Clin Hosp Infant Edo Son 2005; 22 (1)

Obstructive malformations of the aortic arch.

González-Ramos LA, López-Cervantes G, Ruíz-Bustamante NP

Language: Spanish
References: 20
Page: 2-7
PDF size: 315.92 Kb.


ABSTRACT

Introduction: Obstructive anomalies of the aortic arch are a very important group of anatomic malformations that in the neonatal period may originate heart failure cardiogenic shock and early death whether the surgical treatments is not opportune.
Objective: We present our experience with obstructive anomalies of the aortic arch itn our hospital job.
Material and Methods: Both register surgical interventions and autopsia books were reviewed 40 cases of some obstructive anatomic malformations of the aortic arch since 1990 to 2003. Some interest variable were investi-gated as age of the patients clinical features association with other congenital heart defects genetics syndrome and noncardiac malformations in operated patients and autopsied patients.
Results: The anatomic malformation more frecuently founded was aortic coarctation in 35 (87%) cases and interruption of the aortic arch 5 (87%). Clinical charts of the obstructive anomalies of the aortic arch was respi-ratory distress and cyanosis, the systolic murmur was present in 50% and hepatomegaly in 35%. Discrepancy between the amplitude of the pulse in the arms and legs was present in all operated patients and this alteration was reported less frecuently in cases without surgical.
Conclusion: The discrepancy between the amplitude of the pulse in the arms and legs is very important and orient to the diagnosis of aortic coarctation, has the same importance as the auscultation of the heart and exa-minations of blood pressure too.
The operative mortality in 18 patients was exalted 5 (28%) because this patient had acute disproportionate hemodynamic (shock) at diagnosis time in neonatal period and other cardiac malformations and noncardiac.


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