2017, Number 6
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Acta Pediatr Mex 2017; 38 (6)
Pediatric hepatopulmonary syndrome. Case report and a literature review
López-Birlain L, Cuevas-Schacht FJ, Gutiérrez-Morales G, Alva- Chaire AC
Language: Spanish
References: 11
Page: 371-377
PDF size: 1090.46 Kb.
ABSTRACT
The hepatopulmonary syndrome is an infrequent disease in pediatric
population, with an unknown incidence in Mexico. The diagnosis is a
challenge for the clinician due to the presence of many other causes
of hypoxemia in children with chronic liver disease.
Two patients with Hepatopulmonary Syndrome are presented, showing
the variability in both cases and outcome of the disease. First a patient
with chronic liver disease secondary to an autoimmune disease (Systemic
Lupus Erythematosus) with a torpid evolution, then a patient in
which the diagnosis of chronic liver disease was made after the onset
of the respiratory symptoms. In both cases the ideal treatment should
be hepatic transplantation, however it could not be done because of
the low accessibility to this surgical procedure in our country.
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