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2017, Number 5

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Rev Sanid Milit Mex 2017; 71 (5)

Gorham-Stout syndrome. A case report

García PG, Ponce de León-Fernández CJ

Language: Spanish
References: 50
Page: 458-463
PDF size: 484.48 Kb.


ABSTRACT

Introduction: Gorham-Stout syndrome is a malformation of the lymphatic system that occurs mainly in young people; it is non-neoplastic in nature, affects mainly soft and bony tissues, and has a local aggressiveness and unpredictable evolution. Objective: We present the case of a patient with this syndrome and discuss the current therapeutics. Clinical case: It is a 15-year-old male patient who suffers from a right femoral neck trauma fracture: he is operated on and in the postoperative period develops osteolysis in the proximal femur, acetabulum, ilium and ischiopubic bones, obturator muscles, and gluteus maximus muscle; he was treated with bisphosphonates. Discussion: Focused osteolysis, with no apparent cause, especially in children or adolescents, and after discarding other causes of osteolysis, does not point to this syndrome; it is, therefore, considered a diagnosis of exclusion. The histopathological sample is of great help. Being aware of its existence helps us guide the therapeutics and, thus, change the evolution of this disease.


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