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2017, Número 5

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Rev Sanid Milit Mex 2017; 71 (5)


Síndrome de Gorham-Stout. Reporte de un caso

García PG, Ponce de León-Fernández CJ

Idioma: Español
Referencias bibliográficas: 50
Paginas: 458-463
Archivo PDF: 484.48 Kb.


RESUMEN

Introducción: El síndrome de Gorham-Stout es una malformación del sistema linfático que se presenta en jóvenes principalmente; es de carácter no neoplásico y afecta sobre todo los tejidos blandos y óseos; es de agresividad local y su evolución, impredecible. Objetivo: Presentar el caso de un paciente con este síndrome y discutir la terapéutica actual. Caso clínico: Se trata de un paciente masculino de 15 años de edad que sufre una fractura basicervical femoral derecha postraumática; es intervenido quirúrgicamente y en el postoperatorio evoluciona con osteólisis de fémur proximal, acetábulo, ramas ilio- e isquiopúbicas, músculos obturadores y porción inferior del glúteo mayor; es manejado con bifosfonatos. Discusión: La osteólisis focalizada sin causa aparente, especialmente en niños o adolescentes y después de descartar otras causas de la misma, no orienta a este síndrome, por lo que se considera como un diagnóstico por exclusión. La muestra histopatológica es de gran ayuda. El pensar en su existencia ayuda a orientar la terapéutica y cambiar la evolución de la enfermedad.


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