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Academia Mexicana de Neurología, A.C.

2017, Number 1

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Rev Mex Neuroci 2017; 18 (1)

Status epilepticus in a teenager: It is Rassmusen encephalopathy!

Frigerio P, Marcos-Morales S, Peña-Velázquez A, Rosales-Gutiérrez AO, Ortiz-Morales AJ

Language: Spanish
References: 15
Page: 2-8
PDF size: 232.27 Kb.


ABSTRACT

Introduction. Rasmussen encephalitis is a chronic, progressive and inflammatory hemispheric disease of the central nervous system characterized by motor focal seizures resistant to treatment culminating in severe neurological impairment, hemiparesis, aphasia and cognitive impairment.
Case report. The case of a 16-year-old male patient with treatment-resistant continuous motor focal seizures is presented and a description of the disease is discussed for the medical community.
Conclusion. Rasmussen encephalitis should be part of the differential diagnosis in patients with chronic status epilepticus characterized by focal seizures whose clinical picture has begun with encephalopathy with behavioral changes. Early treatment may reduce the number of clinical complications in the long term.


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