Félix-Esquer TA, Muñoz-Valencia ME, Torres-Amaya MA

Language: Spanish
References: 17
Page: 52-55
PDF size: 195.94 Kb.

ABSTRACT

Background. Encephalitis associated with anti-NDMA (N-Metil-D-Aspartate) receptor antibodies, is a rare entity, but is the most frequent cause of autoimmune encephalitis, a condition that affects mainly young women. Objective. Review of the current concepts, diagnosis and management of autoimmune encephalitis. Clinical case. A 13 year old teenage presented to the Emergency Department on two occasions with status epilepticus, that warranted barbituric coma to alleviate the seizures. The patient had no pathological history of importance, and no previous events. The diagnostic approach yielded negative results in all studies made, and in the absence of abnormal findings, a determination of ant-NDMA receptor antibodies in cerebrospinal fluid was included, which resulted positive. The diagnosis of autoimmune encephalitis was made, secondary to the presence of anti-NDMA receptor antibodies. Conclusion. There should be a high clinical suspicion of this pathology in order to guide the diagnosis and treatment approach, since it is a reversible and recoverable condition.

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