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ISSN 0185-3252 (Print)
Revista de la Asociación Médica del Centro Médico ABC

2016, Number 2

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An Med Asoc Med Hosp ABC 2016; 61 (2)

Jeavons syndrome

Cervantes GAI, Navarro BJ, Shkurovich BP

Language: Spanish
References: 18
Page: 137-141
PDF size: 629.19 Kb.


ABSTRACT

Jeavons syndrome, also known as myoclonic epilepsy with absences, is considered a generalized epilepsy characterized by palpebral myoclonus, with or without absences, which are induced with eye closure, pattern of the electroencephalogram with spikes and polyspike-wave discharges, with photosensitivity. Although rare, also tonic-clonic seizure generalized may occur, they tend to occur in patients related to any precipitating factor such as insomnia, alcohol intake, poor adherence to antiepileptic treatment and exposure to light (television, video-games). This feature of photosensitivity tends to decrease with age and can be suppressed with antiepileptic treatment, generally patients have normal intelligence quotient, normal neurological examination with normal neuroimaging studies. The prognosis is considered similar to juvenile myoclonic epilepsy, meriting prolonged or even for life treatment. Some patients presents certain resistance to antiepileptic drugs. We present the case of a female patient of 15 years of age, which began at 7 years old with episodes of flickering that become increasingly constant, at 9 she suffered several episodes of tonic-clonic seizures, without alterations in her physical examination, well controlled with combination therapy with levetiracetam and valproic acid.


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