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2016, Number 1

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Gaceta Médica Espirituana 2016; 18 (1)

Epidermolytic hyperkeratosis. Case presentation

Sánchez LV, Fernández QY, González TA, Saez BN

Language: Spanish
References: 10
Page:
PDF size: 128.65 Kb.


ABSTRACT

Background: The Epidermolytic hyperkeratosis is a genodermatosis with pattern of inheritance dominant autosomal ,it affects equally to both sexes, it is a strange illness and he/she is considered a case each 300 000 people in those that the bladders prevail when being born and the subsequent hyperkeratosis. Objective: To describe the case of a patient with Epidermolytic hyperkeratosis that represents an uncommon clinical situation for their incidence. Case presentation: 17 year-old adolescent, with hyperkeratosis lesions and he/she witnesses of big flakes of dark color that come off easily in big epidermal torn pieces, and that he/she accompanies of fetid scent. Conclusions: This case constitutes an ICHTHYOSIS bullous of Siemens from the clinical point of view, a subtype of Epidermolytic hyperkeratosis, although the alone histology confirms this last one diagnostic.


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