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ISSN 1561-3119 (Electronic)

2015, Number 4

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Rev Cubana Pediatr 2015; 87 (4)

Split spinal cord malformation seen at the neonatal stage

Díaz ÁM, Peña FM, Camejo MM, Céspedes BO, Salinas VME

Language: Spanish
References: 27
Page: 529-536
PDF size: 154.30 Kb.


ABSTRACT

Split spinal cord malformation is a rare form of occult spinal dysraphia and is reported in 3 % of occult dysraphisms which are mainly located in the lumbar region. The Cuban literature made reference to two patients with this condition, an adult and a child. This is the case of a male newborn referred to our center because he presented with occipital meningocele. The examination revealed a small fossa in the sacrococcygeal region, muscular hypotonic in his right lower limb, varus foot and little movement as well as anal and vessical sphincter incontinence. Imaging studies show the presence of two hemicords at the lumbar region, so it is confirmed that this newborn infant had split spinal cord malformation syndrome, which is an uncommon entity. It is interesting to note that this malformation was diagnosed at the neonatal phase because of its clinical manifestations, a relevant aspect since this illness generally shows its symptoms in later life or remains asymptomatic.


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