Méndez-Vivas WR, Vázquez-Pelcastre R, Escalante-San Román A, Pereyra-Balmes MC

Language: Spanish
References: 20
Page: 143-146
PDF size: 490.19 Kb.

ABSTRACT

The Frantz -Gruber tumor is a rare pancreatic pseudopapillary solid mass, and low malignant potential, described in 1959 by Frantz. Predominates in young women between the third and fourth decades of life. The symptomatology is given by the mass effect and is characterized by fullness, early satiety and vomiting and abdominal pain rarely. The radiological diagnosis includes CT, MRI and endoscopic ultrasound; histological studies confirm the clinical suspicion. The approach is surgical in most cases and includes complete tumor resection (distal pancreatectomy plus splenectomy block), presence of liver metastases is rare, 5-year survival is greater than 90%. The case of a patient aged 13, was admitted via pediatric rolling admission with abdominal pain and vomiting, abdominal U.S. shows a mass in the tail of the pancreas confirmed by CT and endoscopic U.S. in which a solid tumor was seen and surgical approach was suggested and smoothly performed during which a solid tumor pending on the body and tail of the pancreas of 11 x 10 cm was found.

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