Morales HJC, Herrera BÁ, Barradas HMI

Language: Spanish
References: 22
Page: 111-116
PDF size: 161.70 Kb.

ABSTRACT

Introduction. The immune-mediated inner ear disease results in less than 1% of hearing loss, and is associated with systemic immune disorders by sex and age. Objective. To present a clinical case of a female patient with right side hearing loss secondary to neonatal hypoxia, left hearing loss of immune etiology and left vestibular schwannoma. Material and methods. Quantitative analysis of hearing and balance to a 47 year old with rapidly progressive hearing impairment adding vestibular symptoms (dizziness and unsteadiness) with good response to steroid treatment is performed. Laboratory parameters are recorded in order to categorize patient etiology. Results. Audiometry: Right ear with audiometric anacusia. Left ear with profound hypoacusia sensorineural curve. Videonystagmography: Dix-Hallpike (+) with cervical traction on both sides. The rest shows no alterations. Posturography: four conditions were performed, showing declines in the fifth and sixth condition. Laboratory tests: (25/05/11): antinuclear, anticentromere, Ac anticytoplasmic: Ac antiphospholipid: anticardiolipin, positive anticardiolipin and after treatment with prednisone 60 mg every 24 hours; these markers became negative. Conclusion. Autoimmune hearing loss is an uncommon condition (‹ 1% of the causes of hearing loss), characterized by recurrent episodes of fluctuating hypoacusia with or without dizziness, vertigo or instability, where it was named autoimmune bony labyrinth disease for it includes the posterior labyrinth. It can be part or not of the clinical context of a systemic autoimmune disease. However "some other concomitant pathology is not exempt" in the same patient.

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