2014, Number 2
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Mediciego 2014; 20 (2)
Prune-Belly Syndrome. A case presentation
Portela RO, Ojeda PB, Luna A, Pino MS, Avello BI, Carrera EL
Language: Spanish
References: 20
Page:
PDF size: 105.53 Kb.
ABSTRACT
The Prune-Belly syndrome is a distinct entity of unknown etiology, consisting of a spectrum of
congenital malformations able to lead the pregnancy to abortion, or post-natal complications
usually urinary of varying degrees of morbidity / mortality, which will determine the outcome
of the infant born with this condition. Although it is a clinical picture with a very low mortality,
the consequences are different for health and quality of infants life. In this research a case of
Prune-Belly that was born at 36 weeks gestation, who presented the classic findings of this
rare syndrome is reported.
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