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ISSN 0210-5187 (Electronic)

2013, Number 5

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Med Cutan Iber Lat Am 2013; 41 (5)

Bart syndrome: congenital aplasia cutis and epidermolysis bullosa

Luján SM, García GRG, Álvarez CJP, Uribe PCJ

Language: Spanish
References: 14
Page: 218-222
PDF size: 667.73 Kb.


ABSTRACT

Aplasia cutis has been associated with the main subtypes of bullous epidermolysis, receiving the name of Bart syndrome. It mainly affects one lower limb with a characteristic absence of skin with a S-shaped pattern plus bullous epidermolysis lesions elsewhere in the body. We present the case of a pre-term male infant with all the clinical features mentioned investigated in the Neonatology Service of the Fundación Cardiovascular de Colombia, Floridablanca, Colombia.


REFERENCES

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