2014, Number 1
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Rev Cubana Pediatr 2014; 86 (1)
Atypical case of juvenile idiopathic osteoporosis
Hernández GI, Bustamante TM, Rodríguez OM, León PS, García GA
Language: Spanish
References: 10
Page: 108-114
PDF size: 131.86 Kb.
ABSTRACT
Juvenile idiopathic osteoporosis is a disease seen in children and adolescents, it is self-limited, characterized by axial and limb osteoporosis, occasionally related to vertebral collapse, which finally resulted in thoracic kyphosis. To date, the association between this disease and dental impairments is not known. Here is the case of a male adolescent, with history of delayed change to permanent dentition and osteopenia; he was evaluated by several medical specialists as internal medicine, odontology, orthopedics, endocrinology and nephrology. He was diagnosed as juvenile idiopathic osteoporosis case, and on the basis of the symptom picture and the numerous supplementary tests, it was possible to rule out several hereditary and acquired illnesses such as late imperfect osteogenesis and hyperparathyroidism. This case stressed the presence of dentition impairments and little vertebral effect.
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