Martínez GG, Pozo AD, Rodríguez MH

Language: Spanish
References: 13
Page: 619-625
PDF size: 76.46 Kb.

ABSTRACT

Introduction: chronic Cor Pulmonale is a syndrome characterized by pulmonary hypertension and failure of right heart secondary to a variety of primary diseases of the pleura, lungs, chest wall and pulmonary circulation. His relationship with the final phase of infiltrative lung disease is well described in the literature.
Objectives: to describe an unusual case of chronic cor pulmonale pulmonary fibrosis in a young patient with no history of progressive dyspnea.
Case: young woman of 35 who entered the hospital with dyspnea, abdominal pain and severe lower limb edema. On physical examination was found also heart murmur, jugular venous distension and hepatomegaly failure. CT was performed transthoracic lung which was diagnosed right heart failure and severe pulmonary fibrosis.
Conclusions: radiological and echocardiographic study demonstrated the presence of chronic Cor Pulmonale due to acute interstitial pneumonitis.

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