2013, Number 4
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Rev Mex Anest 2013; 36 (4)
Noonan syndrome and malignant hyperthermia risk: total intravenous anesthesia for pediatric outpatient surgery
Ramírez-Paesano CR, Hachoue-Saliba ZS
Language: Spanish
References: 19
Page: 314-318
PDF size: 245.88 Kb.
ABSTRACT
The Noonan syndrome is a clinical entity that could be confused or related to other syndromes associated with the development of malignant hyperthermia. In order to avoid the appearance of a malignant hyperthermia crisis, the anesthetic technique should be free of triggering agents and patients should be adequately monitored. In this report we describe a child patient with probable Noonan syndrome and anesthetic management to cryptorchidism repair.
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