Ramírez-Paesano CR, Hachoue-Saliba ZS

Idioma: Español
Referencias bibliográficas: 19
Paginas: 314-318
Archivo PDF: 245.88 Kb.

RESUMEN

El síndrome de Noonan es una entidad clínica que puede confundirse o estar relacionada con otros síndromes asociados con el desarrollo de hipertermia maligna. Con el fin de evitar la aparición de una crisis de hipertermia maligna, la técnica anestésica debe ser libre de agentes desencadenantes y contar con la monitorización adecuada. En este reporte se presenta el caso de un paciente escolar con síndrome de Noonan y el manejo anestésico para la cirugía de reparación de criptorquidia.

REFERENCIAS (EN ESTE ARTÍCULO)

1. Benca J, Hogan K. Malignant hyperthermia, coexisting disorders, and enzymopathies: risks and management options. Anesth Analg. 2009;109:1049-1053.

2. Tartaglia M, Gelb B, Zenker M. Noonan syndrome and clinically related disorders. Best Pract Res Clin Endocrinol Metab. 2011;25:161-179.

3. Aggarwal V, Malik V, Malhotra KP, Kiran U. Noonan syndrome: an anesthesiologist’s perspective. Annals Cardiac Anaesthesia. 2011;14:214-217.

4. Bentires AM, Kontaridis MI, Neel BG. Stops along the RAS pathway in human genetic disease. Nat Med. 2006;12:283-285.

5. Tidyman WE, Rauen KA. The RAS apathies: developmental syndromes of RAS/MAPK pathway dysregulation. Curr Opin Genet Dev. 2009;19:230-236.

6. Litman R. Management of malignant hyperthermia and malignant hyperthermia–susceptible patients in the ambulatory setting. ASA Refresher Courses in Anesthesiology. 2011;39:86-91.

7. Lee CK, Chang BS, Hong YM, Yang SW, Lee CS, Seo JB. Spinal deformities in Noonan syndrome: a clinical review of sixty cases. J Bone Joint Surg. 2001;83:1495–1502.

8. Hunter A, Pinsky L. An evaluation of the possible association of malignant hyperpyrexia with the Noonan syndrome using serum creatine phosphokinase levels. J Pediatr. 1975;86:412-415.

9. D’Arcy CE, Bjorksten A, Yiu EM, et al. King-Denborough syndrome caused by a novel mutation in the ryanodine receptor gene. Neurology. 2008;71:776–777.

10. Noonan syndrome guideline development group. Management of Noonan syndrome-a clinical guideline[Internet]. UK: University of Manchester DYSCERNE; 2010 [Accessed 25 July 2011].

11. Mani V, Morton N. Overview of total intravenous anesthesia in children. Pediatric Anesthesia. 2010;20:211-222.

12. McCormack J. Total intravenous anesthesia in children. Current Anaesthesia & Critical Care in Press. 2008;1-6.

13. Wilson G. Target controlled infusion anesthesia in children. S Afr J Anaesthesiol Analg. 2010;16:124-126.

14. Ong C, Seymour R, Lirk P, Merry A. Combining paracetamol (acetaminophen) with nonsteroidal antiinflammatory drugs: a qualitative systematic review of analgesic efficacy for acute postoperative pain. Anesth Analg. 2010;110:1170-1179.

15. Zaragoza LG, Mejía TG, Peralta ZE. Bloqueo de nervios periféricos guiados por ultrasonido. Rev Mex Anestesiol. 2008;31:282-297.

16. Bermúdez E. Bloqueos de la pared abdominal. Rev Chil Anest. 2011;40:230-237.

17. Suresh S, Chan V. Ultrasound guided transverses abdominis plane block in infants, children and adolescents: a simple procedural guidance for their performance. Pediatric Anesthesia. 2009;19:296-299.

18. Siddiqui M, Sajid M, Uncles D, Cheek L, Baig M. A meta-analysis on the clinical effectiveness of transverses abdominis plane block. Journal of Clinical Anesthesia. 2011;23:7-14.

19. Klockars J, Hiller A, Ranta S, Talja P, van Gils M, Taivainen T. Spectral entropy as a measure of hypnosis in children. Anesthesiology. 2006;104:708-717.