2013, Number 2
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Rev Mex Angiol 2013; 41 (2)
Síndrome de Parkes Weber; Schobinger IV
Sierra-Juárez MÁ, Córdova-Quintal P, Fabián-Mijangos W, Campero-Urcullo A, Zamora-García C
Language: Spanish
References: 6
Page: 78-81
PDF size: 252.89 Kb.
ABSTRACT
The Parkes Weber syndrome is an overgrowth of a limb related to the presence of multiple arteriovenous
fistulas along a limb affected, commonly affects the lower extremities. The case of male patient
aged 29 who goes to the vascular surgery service for presenting ulcer on the external face of the right leg
which is actively bleeding and dyspnea. Surgical procedure is performed resected proximal fistulas arteriovenous
with a femoral bypass graft. For patients with severe complications that compromise the
life or limb, can benefit from the partial removal of the lesions, however may result in recurrence; that
be more difficult to handle than the initial deformity.
REFERENCES
Alomari A, Josée Dubois J. Interventional Management of Vascular Malformations. Tech Vasc Interventional Rad 2011; 14: 22-31.
Revencu N, Boon LM, Mulliken JB, Enjolras O, Cordisco MR, Burrows PE, et al. Parkes Weber syndrome, vein of Galen aneurismal malformation, and other fast-flow vascular anomalies are caused by RASA1 mutations. Human Mutation 2008; 29(7): 959-65.
Corstiaan C, Maruschka P, Merkusb J. Henk Sillevis Smittc, Dink A. Quality of life in patients with vascular malformations of the lower extremity. The British Association of Plastic Surgeons 2004; 57: 754-63.
Picolini A, Carlessi A, Heredia G, Moles V, Molinas H, Alaguibe E. Insuficiencia cardíaca de alto gasto por fístula arterio-venosa congénita. Síndrome de Parkes Weber. Insuf Card 2010; 5(3): 150-3.
Suzuki T, Miyata K, Hoshina H, Okamoto H, Kimura. Surgical treatment of patients with congenital vascular malformation-associated aneurysms. Eur J Vasc Endovasc Surg 2011; 42: 517e-522e.
Garzon MC, Huang JT, Enjolras O, Frieden IJ. Vascular malformations. Part II: Associated syndromes. J Am ACAD Dermatol 2007; 56 (4): 541-64.