medigraphic.com

2010, Number 3

<< Back Next >>

Rev Hosp Jua Mex 2010; 77 (3)

Quistes hepáticos múltiples no asociados a poliquistosis renal. Revisión de la literatura y presentación de un caso clínico

López MH, Pardo CR, Miramontes AC, López ZC

Language: Spanish
References: 14
Page: 216-219
PDF size: 256.36 Kb.


ABSTRACT

The polycystic liver disease (PLD) is an autosomal-dominant pathology that presents in the adult life. Rarely symptomatic, patients with PLD usually require little intervention. However, the prevalence of polycystic liver disease associated to kidney disease has undoubtedly contributed to the large number of cases of symptomatic hepatomegaly reported in the medical literature. Isolated polycystic liver disease is underdiagnosed and genetically distinct from polycystic liver disease associated with autosomal dominant polycystic kidney disease (ADPKD) but with similar pathogenesis and clinical manifestations. We report a case of a female patient who presents polycystic liver disease not relationated to kidney polycystic disease.


REFERENCES

  1. Redston MS, Wanless IR. The hepatic von Meyenburg complex: Prevalence and association with hepatic and renal cysts among 2,843 autopsies [corrected] [erratum appears in Mod Pathol 1996 Jul; 9(7): 803]. Mod Pathol 1996; 9: 233-7.

  2. Pirson Y, Lannoy N, Peters D, Geubel A, Gigot JF, Breuning M, Verellen-Dumoulin C. Isolated polycystic liver disease as a distinct genetic disease, unlinked to polycystic kidney disease 1 and polycystic kidney disease 2. Hepatology 1996; 23: 249- 52.

  3. Kerkar N, Norton K, Suchy FJ. The Hepatic Fibrocystic Diseases Bristowe F. Cystic disease of the liver associated with a similar disease of the kidneys. Trans Pathol Soc Lond 1856; 7: 229-34. Clin Liver Dis 10 (2006) 55-71.

  4. Sierra EE, Vázquez RJ, Martínez RG. Quistes solitarios no parasitarios del hígado. Presentacion de nueve casos. Rev Cubana Cir 1999; 38: 109-16.

  5. Haddad Ar, West BKC, Graham GG, Morris WD, Campbell GS. Syntomatic nonparasitic liver cyst. Am J Surg 1977; 134: 739-44.

  6. Ortíz GJ, Gracida MNI, Sánchez LR, Reyes SMP. Quistes hepáticos no parasitarios. Cir Gen 2002; 24: 326-34.

  7. Somlo S, Torres VE, Reynolds D, King BF, Nagorney DM: Autosomal dominant polycystic liver disease without polycystic kidney disease is not linked to either the PKD1 or PKD2 gene loci [abstract]. J Am Soc Nephrol 1995; 6: 727A.

  8. Leier CV, Baker PV, Kilman JW, et al. Cardiovascular abnormalities associated with adult polycystic kidney disease. Ann Intern Med 1984; 100: 683-8.

  9. Melnick P. Polycystic liver: Analysis of 70 cases. Arch Pathol 1955; 59: 162–72.

  10. Arnold HL, Harrison SA. New Advances in Evaluation and Management of Patients with Polycystic Liver Disease. Am J Gastroenterol 2005; 100: 2569- 82.

  11. Desmet V. Congenital diseases of intrahepatic bile ducts: Variations on the theme “ductal plate malformation.” Hepatology 1992; 16: 1069-83.

  12. Ueda M, Egawa H, Oike F, et al. Living donor liver transplantation for polycystic liver disease. Transplantation 2004; 77: 480-1

  13. Fiamingo P, Tedeshi U, Veroux M, et al. Laparoscopic Treatment for simple hepatic cysts and polycystic liver disease. Surg Endosc 2003; 17: 623-6.

  14. Yang GS, Li QG, Lu JH, et al. Combined hepatic resection with fenestration for highly syntomatic polycystic liver disease. A report for 7 patients. World J Gastroenterol 2004; 10: 2598-601.




2020     |     www.medigraphic.com