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ISSN 0187-5337 (Print)
Instituto Nacional de Perinatología

2013, Number 1

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Perinatol Reprod Hum 2013; 27 (1)

Extensive Paget's disease of the vulva: Report of a case and conservative management proposal

Márquez-Acosta G, Olaya-Guzmán EJ, Jiménez-López J, Gómez-Pue D, Pérez-Quintanilla M

Language: Spanish
References: 26
Page: 44-50
PDF size: 388.05 Kb.


ABSTRACT

Extramammary Paget’s disease (EPD) is a malignant disease observed, especially in areas with high density of apocrine glands. We report a case of a patient of 68 years old, attended at the Colposcopy Clinic of Oncology, National Institute of Perinatology Isidro Espinosa de los Reyes, diagnosed with Paget’s disease of the vulva, vagina, perineum region and perianal region, and managed with laser vaporization sessions with satisfactory outcome. Since it is a rare disease, more common in females and in whites, with the highest incidence in the seventh decade of life, as is the case of our patient, propose in this paper to present a review of the clinical evaluation with emphasis on the differential diagnosis, use of colposcopy for diagnosis and dividing up conservative treatment with laser vaporization of the disease. The low incidence of Paget’s disease of the vulva, vagina, perineum and perianal region, and the absence of reports on the possibility of nonsurgical treatment encouraged to inform the scientific community about the management with laser vaporization, with the intention of avoiding morbidity that can lead to the conventional surgical maneuvers.


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