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2002, Number 1

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Rev Med Hosp Gen Mex 2002; 65 (1)

Pancreatic serous cystoadenoma (microcystic adenoma). Report of seven cases

Aristi UG, Güereña EA, Ramos CR

Language: Spanish
References: 53
Page: 15-22
PDF size: 180.01 Kb.


ABSTRACT

Cystic neoplasms of the pancreas constitute an important group of tumors, although they are uncommon, they have a distinctive clinical presentation, indolent biological behavior and a high frequency of successful surgical management. The distinction between non-neoplastic and neoplastic cysts, and between the different types of cystic neoplasms is of considerable clinical importance. The most common cystic neoplasms of the pancreas are the serous cystadenomas (38%). However, they are rare, and not familiar to us; so preoperative diagnosis is often incorrect. This is a descriptive and retrospective study of autopsy and surgical pathology specimens during 10 year period (1991-2000). We found 7 cases of serous pancreatic cystadenomas, five at autopsy, and two in surgical pathology material, all of them in adults (100%), with female predominance (71.4%). Most were incidental findings at autopsy (71.4%), and single lesions (71.4%), except those associated with von Hippel-Lindau disease (two cases). In none was the clinical diagnosis correct. The association with von Hippel-Lindau disease is one of the most characteristic aspects of this tumor. Complete surgical resection is curative and is the treatment of choice. Drainage is not adequate treatment.


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